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Bronchopulmonary foregut malformations

DA: 866




Developmental anomaly information

Definition: Congenital bronchopulmonary foregut malformations are very rare anomalies that result in a communication between the esophagus and a sequestered part of the lung.The term 'bronchopulmonary foregut malformation' was coined by Gerle et al. in 1968. It includes a variety of congenital malformations, including pulmonary sequestration, foregut duplication cysts, and esophageal diverticula. It was left to Heithoff et al.to emphasize that these rare anomalies provide evidence of a common pathogenesis for the whole gamut of bronchopulmonary foregut malformations, which includes intralobar and extralobar sequestrations with or without communications with the alimentary tract, foregut duplication cysts, and esophageal diverticula. Srikanth et al. proposed an anatomical classification for bronchopulmonary foregut malformations and introduced the term 'communicating bronchopulmonary foregut malformations . Communicating bronchopulmonary foregut malformations (CBPFM) are rare abnormalities of the development of the primitive foregut that result in an abnormal communication between the upper gastrointestinal tract and pulmonary tissue. They usually occur in isolation, but sometimes are seen in association with oesophageal atresia (OA).


Synonyms:

  • Communicating bronchopulmonary foregut malformations (CBPFM)


Developmental anomaly parent: (empty)

Topology: Human body > Thorax > Mediastinum

System: Human body > Respiratory system

Developmental anomaly category: Malformation

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Observed in MDB cases
Observed in combinaisons (MDB)
Observed in malformative diseases (MDB)
Associated genes in profile
Associated genes in malformative diseases
Associated chromosomal diseases
Associated signaling pathways
Associated developmental anomalies

Last modified: 2008-12-30 20:14:12 by farideh

Created: 2008-12-30 19:49:11 by



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