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Right aortic arch

DA: 44

Developmental anomaly information

Definition: Right aortic arch is when aortic arch lying to the right of the trachea and oesophagus. Infrequently, the right arch passes to the left side higher in the thorax so that it courses behind and compresses the trachea. This is called a retrotracheal aortic arch. There are two types of right aortic arch: mirror image and nonmirror image. Mirror image has a left innominate artery originating as the first branch of the right arch. This type is nearly always associated with cyanotic congenital heart disease, especially tetralogy of Fallot, pulmonary atresia with ventricular septal defect and truncus arteriosus,(due to third and fourth brachialarch defects). Nonmirror-image right aortic arch usually has the left subclavian artery originating as the fourth branch of the aorta. It originates from the proximal descending aorta with a prominent diverticulum at the site of origin and a course behind the oesophagus. Rare variant types exist such as right arch with left subclavian artery unattached to the aorta but connected to the left pulmonary artery by a ductus arteriosus. Right aortic arch with aberrant left subclavian artery produces a vascular ring with compression of the oesophagus and/or airway. Nonmirror-image arch is infrequently associated with other congenital cardiac anomalies.

Developmental anomaly parent: (empty)

Topology: Human body > Thorax > Mediastinum > Heart and great vessels > Great vessels > Thoracic aorta

System: Human body > Cardiovascular system > Vessels > Arteries > Aorta

Developmental anomaly category: Malformation

Case records MDB138, MDB418, MDB444, MDB457, MDB513, MDB518, MDB235, MDB409

Humpath: 13350

Observed in MDB cases
Observed in combinaisons (MDB)
Observed in malformative diseases (MDB)
Associated genes in profile
Associated genes in malformative diseases
Associated chromosomal diseases
Associated signaling pathways
Associated developmental anomalies

Here is the list of developmental anomalies associated with this developmental anomaly, based on the cases' information :

Last modified: 2008-12-19 22:42:37 by farideh

Created: 2008-02-22 01:00:00 by phsaw

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